Portland State University. Department of Speech Communication
James F. Maurer
Date of Award
Master of Science (M.S.) in Speech: Emphasis in Speech Pathology/Audiology
1 online resource (115 p.)
Monge family, Deafness -- Genetic aspects
The audiological characteristics of the Monge family of Costa Rica were investigated in a sample of fifty-two affected members and twelve unaffected members. Through laboratory analysis by staff personnel from the University of Costa Rica and audiological test results obtained in the present investigation, it was concluded that affected Monge members demonstrate a slowly progressive low frequency sensorineural hearing loss of autosomal dominant transmission. The initial site of lesion appears to be the apical portion of the cochlea, with significant onset occurring during early childhood following normal speech and language acquisition. The rate at which the hearing loss progresses and the frequency regions affected are contingent upon chronological age, culminating in a flat profound hearing impairment by age thirty for all affected members.
Moulton, Christine, "Audiological characteristics of the Monge family of Costa Rica" (1983). Dissertations and Theses. Paper 3343.